abstract：OBJECTIVE:To evaluate the family psycho-social outcomes of children with Down syndrome and atrioventricular septal defect, and examine the impact of these variables on the child's neurodevelopmental outcome. METHODS:This was a cross-sectional study that consisted of 57 children with Down syndrome - 20 cases and 37 con...

journal_title：Cardiology in the young

authors： Visootsak J,Huddleston L,Buterbaugh A,Perkins A,Sherman S,Hunter J

更新日期：2016-02-01 00:00:00

abstract：OBJECTIVES:The bi-directional cavopulmonary anastomosis forms an essential staging procedure for univentricular hearts. This review aims to identify risk factors for morbidity, mortality, and suitability for Fontan completion. METHODS:A total of 114 patients undergoing cavopulmonary anastomosis between 1992 and 2012 w...

journal_title：Cardiology in the young

authors： François K,Vandekerckhove K,De Groote K,Panzer J,De Wolf D,De Wilde H,Bové T

更新日期：2016-02-01 00:00:00

abstract：:We present a case of circumferential fracture of aortic coarctation stent with severe re-stentosis presenting 16 years after initial stent implantation with end-stage renal disease. The patient was treated with a covered stent using the stent-in-stent technique. The use of an ultra-high-pressure balloon was proved nec...

journal_title：Cardiology in the young

authors： Ayoub F,AlShelleh S,A L-Ammouri I

更新日期：2016-02-01 00:00:00

abstract：:We report the case of a 12-day-old newborn affected by coarctation of the aorta and intraventricular defect who underwent coarctectomy and pulmonary artery banding. On post-operative day 7, the patient suffered from pulseless electric activity due to tension pneumothorax. Point-of-care ultrasound was performed during ...

journal_title：Cardiology in the young

authors： Polito A,Biasucci DG,Cogo P

更新日期：2016-02-01 00:00:00

abstract：BACKGROUND:The physiological importance of the lateral tunnel stenosis in the Fontan pathway for children with single ventricle physiology can be difficult to determine. The impact of the stenosis and stent implantation on total cavopulmonary connection resistance has not been characterized, and there are no clear guid...

journal_title：Cardiology in the young

authors： Tang E,McElhinney DB,Restrepo M,Valente AM,Yoganathan AP

更新日期：2016-01-01 00:00:00

abstract：:Children with a secundum atrial septal defect are usually asymptomatic and are referred for elective closure after 3-4 years of age; however, in premature infants with chronic lung disease, bronchopulmonary dysplasia, or pulmonary hypertension, increased pulmonary blood flow secondary to a left-to-right atrial shunt, ...

journal_title：Cardiology in the young

authors： Zussman ME,Freire G,Cupp SD,Stapleton GE

更新日期：2016-01-01 00:00:00

abstract：:Berry syndrome is a rare CHD. Approximately 29 cases have been described in the literature. Surgical correction has been successfully performed as well. We report the case of a newborn diagnosed with Berry syndrome who was subsequently diagnosed with trisomy 13. Cytogenetic analysis should be performed before surgical...

journal_title：Cardiology in the young

authors： Remon JI,Briston DA,Stern KW

更新日期：2016-01-01 00:00:00

abstract：:D is an 8-year-old boy brought to his paediatrician for evaluation. His mother is concerned as his teacher has been frequently complaining that he is very restless and often disturbs the rest of the class by getting up on some pretext or the other. He is unable to concentrate on his work and gets distracted very easil...

journal_title：Cardiology in the young

authors： Aggarwal V,Aggarwal A,Khan D

更新日期：2016-01-01 00:00:00

abstract：:A newborn presented with an aorto-right ventricular tunnel, a defect connecting the left aortic sinus to the right ventricle. The patient underwent repair on 4th day of life. ...

journal_title：Cardiology in the young

authors： Ziesenitz VC,Gorenflo M,Loukanov T

更新日期：2016-01-01 00:00:00

abstract：:An infant presented with features suggestive of an anomalous left coronary artery was found to have normal origins of both coronary arteries. Echocardiography during episodes of ischaemia showed marked aortic regurgitation with retrograde coronary flow. The left coronary leaflet was mildly hypoplastic. Surgical re-sus...

journal_title：Cardiology in the young

authors： Likes ML,Silverman NH,Albers EL,Choy R,Bhat A,McMullan DM

更新日期：2015-12-01 00:00:00

abstract：UNLABELLED:Introduction The optimal perioperative feeding strategies for neonates with CHD are unknown. In the present study, we describe the current feeding practices across a multi-institutional cohort. METHODS:Inclusion criteria for this study were as follows: all neonates undergoing cardiac surgery admitted to the...

journal_title：Cardiology in the young

authors： Alten JA,Rhodes LA,Tabbutt S,Cooper DS,Graham EM,Ghanayem N,Marino BS,Figueroa MI,Chanani NK,Jacobs JP,Donohue JE,Yu S,Gaies M

更新日期：2015-12-01 00:00:00

abstract：:Atrioventricular valve regurgitation is widely known as a risk factor for Fontan completion in patients with univentricular physiology. To date, indications and timing for atrioventricular valve repair remain unclear and different surgical techniques have been advocated. Since 2013, 50 consecutive patients underwent e...

journal_title：Cardiology in the young

authors： Gil-Jaurena JM,González-López MT,Pérez-Caballero R,Pita A

更新日期：2015-10-01 00:00:00

abstract：:The aims of this study were to assess the development of heart failure in patients with congenitally corrected transposition of the great arteries in a medium-term follow-up, to identify the impact of tricuspid regurgitation on the development of heart failure, and to determine the most reliable marker for its identif...

journal_title：Cardiology in the young

authors： Koželj M,Cvijić M,Berden P,Podnar T

更新日期：2015-10-01 00:00:00

abstract：:Primary vascular tumour of the heart is rare, especially in neonates and infants. We report a male premature newborn with a right atrial tumour associated with a large amount of pericardial effusion detected by screening foetal echography. Diagnosis of capillary haemangioma was confirmed by histopathological examinati...

journal_title：Cardiology in the young

authors： Lin TW,Wang JN,Kan CD

更新日期：2015-10-01 00:00:00

abstract：OBJECTIVE:Arrhythmias are common in patients admitted to the paediatric intensive care unit. We sought to identify the rates of occurrence and types of arrhythmias, and determine whether an arrhythmia was associated with illness severity and paediatric intensive care unit length of stay. DESIGN:This is a prospective, ...

journal_title：Cardiology in the young

authors： Cassel-Choudhury GN,Aydin SI,Toedt-Pingel I,Ushay HM,Killinger JS,Cohen HW,Ceresnak SR

更新日期：2015-10-01 00:00:00

abstract：:A 31-year-old patient previously underwent a Mustard operation presented with palpitations. Atrial tachycardia and paroxysmal atrial fibrillation were documented on the surface electrocardiogram. Under the guidance of a three-dimensional electroanatomic mapping system, ablation of the isolated left-sided pulmonary vei...

journal_title：Cardiology in the young

authors： Ban JE,Park SW,Kim YH

更新日期：2015-08-01 00:00:00

abstract：BACKGROUND:CHD is the leading cause of mortality due to birth defects. Array comparative genomic hybridisation (aCGH) detects submicroscopic copy number changes and may improve identification of the genetic basis of CHD. METHODS:This is a retrospective analysis of 1252 patients from a regional referral centre who had ...

journal_title：Cardiology in the young

authors： Hightower HB,Robin NH,Mikhail FM,Ambalavanan N

更新日期：2015-08-01 00:00:00

abstract：:Heart failure in children is a complex clinical syndrome with multiple aetiologies. The underlying disorders that lead to heart failure in children differ significantly from those in adults. Some clinical biomarkers for heart failure status and prognosis appear to be useful in both age groups. This review outlines the...

journal_title：Cardiology in the young

authors： Xu M,Ramirez-Correa GA,Murphy AM

更新日期：2015-08-01 00:00:00

abstract：:Paediatric heart transplantation has evolved over the last 3 decades. The research group, Pediatric Heart Transplant Study, has been in step with that evolution over the nearly 20 years of its existence by utilising its registry to contribute a wealth of clinical research to the field. The highlights of its studies wi...

journal_title：Cardiology in the young

authors： Law YM

更新日期：2015-08-01 00:00:00

abstract：BACKGROUND:Although some prior studies have provided evidence to question the historical belief that pulmonary vascular resistance index ⩾6 Wood Units×m2 should be a contraindication to heart transplantation in children, no national analyses specific to the modern area have addressed this question. METHODS:Data were a...

journal_title：Cardiology in the young

authors： Maxwell BG,Sheikh AY,Ajuba-Iwuji CC,Heitmiller ES,Vricella LA

更新日期：2015-08-01 00:00:00

abstract：INTRODUCTION:Subclinical hypothyroidism or mild thyroid failure is a common problem in patients without known thyroid disease. METHODS:Demographic and analytical data were collected in 309, of which 181 were male and 128 were female, congenital heart disease (CHD) patients. CHD patients with thyroid-stimulating hormon...

journal_title：Cardiology in the young

authors： Martínez-Quintana E,Rodríguez-González F

更新日期：2015-08-01 00:00:00

abstract：BACKGROUND:Altered mesenteric perfusion may be a contributor to the development of necrotising enterocolitis in patients with hypoplastic left heart syndrome. The goal of this study was to document mesenteric flow patterns in patients with hypoplastic left heart syndrome pre- and post-hybrid procedure. METHODS:A prosp...

journal_title：Cardiology in the young

authors： Cozzi CT,Galantowicz M,Cheatham JP,Nicholson L,Fernandez R,Backes CH,McCaw C,Cua CL

更新日期：2015-08-01 00:00:00

abstract：BACKGROUND:Holt-Oram syndrome is characterised by CHD and limb anomalies. Mutations in TBX5 gene, encoding the T-box transcription factor, are responsible for the development of Holt-Oram syndrome, but such mutations are variably detected in 30-75% of patients. METHODS:Clinically diagnosed eight Holt-Oram syndrome pat...

journal_title：Cardiology in the young

authors： Jhang WK,Lee BH,Kim GH,Lee JO,Yoo HW

更新日期：2015-08-01 00:00:00

abstract：OBJECTIVE:To assess haemodynamic patterns in head-up tilt testing on 400 paediatric cases with unexplained syncope. METHODS:Medical records of 520 children who underwent head-up tilt testing in the preceding year were retrospectively evaluated, and 400 children, 264 (66%) girls and 136 (34%) boys, aged 12.6±2.6 years ...

journal_title：Cardiology in the young

authors： Yozgat Y,Karadeniz C,Ozdemir R,Doksoz O,Kucuk M,Karaarslan U,Mese T,Unal N

更新日期：2015-06-01 00:00:00

abstract：:Anomalous origin of the right coronary artery from the posterior, non-coronary sinus is extremely rare and has never been reported in a paediatric-age competitive athlete. We report this very rare case of the right coronary artery arising from the posterior sinus. In the anomalous right coronary from the posterior sin...

journal_title：Cardiology in the young

authors： Adebo D,Jacobson Z,Harris MA

更新日期：2015-06-01 00:00:00

abstract：INTRODUCTION:The diagnosis of trisomy 21 in children has been associated with failed extubation after CHD surgery. Dexmedetomidine may be a useful agent to improve postoperative outcomes in these patients, such as ventilator time, ICU length of stay, or hospital length of stay. MATERIALS AND METHODS:The Pediatric Heal...

journal_title：Cardiology in the young

authors： Moffett BS,Mossad EB,Tobias JD,Cabrera AG

更新日期：2015-06-01 00:00:00

abstract：AIM:We aimed to investigate the role of adiponectin in acute rheumatic fever by evaluating correlations with cytokines and acute-phase reactants. METHODS:Patients were divided into three groups by clinical findings. Group 1 included 8 patients with only chorea, Group 2 included 13 patients with arthritis and carditis,...

journal_title：Cardiology in the young

authors： Ozgen H,Ucar B,Yildirim A,Colak O,Bal C,Kilic Z

更新日期：2015-06-01 00:00:00

abstract：OBJECTIVES:To evaluate long-term outcome of initial aortic valve intervention in a paediatric population with congenital aortic stenosis, and to determine risk factors associated with reintervention. PATIENTS AND METHODS:From 1985 to 2009, 77 patients with congenital aortic stenosis and a mean age of 5.8±5.6 years at ...

journal_title：Cardiology in the young

authors： Hochstrasser L,Ruchat P,Sekarski N,Hurni M,von Segesser LK

更新日期：2015-06-01 00:00:00

abstract：:Common arterial trunk with arch obstruction is a rare conotruncal abnormality. We report, with confirmatory images, a neonate with this anomaly and additional supracardiac partial anomalous pulmonary venous connection, as well as phenylketonuria. ...

journal_title：Cardiology in the young

authors： Ayyildiz P,Kasar T,Güzeltas A

更新日期：2015-06-01 00:00:00

abstract：:Percutaneous treatment of aortic coarctation is a widely used option. Covered stents have increased the profile of efficacy and safety of this procedure. Here we report on a 32-year-old woman with significant aortic recoarctation associated with aortic wall aneurysm and close proximity of both lesions to the origin of...

journal_title：Cardiology in the young

authors： Butera G,Piazza L

更新日期：2015-04-01 00:00:00

abstract：:It is controversial to observe or close symptomatic congenital coronary artery fistula in infants. We herein describe a medium-sized symptomatic congenital coronary artery fistula that underwent rapid spontaneous closure in an infant aged <3 months. ...

journal_title：Cardiology in the young

authors： Lu WH,Huang TC,Hsieh KS

更新日期：2015-04-01 00:00:00

abstract：:May-Thurner syndrome is a rare clinical entity involving venous obstruction of the left lower extremity. The May-Thurner syndrome is a phenomenon commonly described as an acquired stenosis of the left common iliac vein secondary to compression of the left common iliac vein between the right common iliac artery and the...

journal_title：Cardiology in the young

authors： Vijayalakshmi IB,Setty HS,Narasimhan C

更新日期：2015-04-01 00:00:00

abstract：BACKGROUND:Disagreement currently exists regarding the definition of aortic dextroposition. It is suggested that the term be used interchangeably with aortic overriding, along with suggestions that the aortic valve overrides in the normal heart. The dextroposed aorta, however, does not always override the crest of the ...

journal_title：Cardiology in the young

authors： Anderson RH,Spicer DE,Henry GW,Rigsby C,Hlavacek AM,Mohun TJ

更新日期：2015-04-01 00:00:00

abstract：:Fibrates are peroxisome proliferator-activated receptor-α agonists and are clinically used for treatment of dyslipidemia and hypertriglyceridemia. Fenofibrate is reported as a cardioprotective agent in various models of cardiac dysfunction; however, limited literature is available regarding the role of gemfibrozil as ...

journal_title：Cardiology in the young

authors： Singh AP,Singh R,Krishan P

更新日期：2015-04-01 00:00:00

abstract：:A two-year-old boy with a background history of Down syndrome and partial atrioventricular septal defect presented with acute respiratory distress requiring intubation and mechanical ventilation. He continued to deteriorate, despite ventilation; direct laryngoscopy, bronchoscopy, and computed tomography demonstrated s...

journal_title：Cardiology in the young

authors： Kelleher EM,Nolke L,McMahon CJ

更新日期：2015-03-01 00:00:00

abstract：UNLABELLED:Physical activity tends to be lower in school-age children with congenital heart disease than in healthy controls. To the best of our knowledge, objectively measured physical activity levels of preschool-age children with congenital heart disease have not been studied. METHODS:A total of 10 children with ei...

journal_title：Cardiology in the young

authors： Stone N,Obeid J,Dillenburg R,Milenkovic J,MacDonald MJ,Timmons BW

更新日期：2015-03-01 00:00:00

abstract：:We report a left atrial appendage diverticulum in close proximity to the left coronary artery, thereby mimicking a fistulous connection between the two structures. ...

journal_title：Cardiology in the young

authors： Cantinotti M,Giordano R,Murzi B

更新日期：2015-03-01 00:00:00

abstract：:Interest in brain natriuretic peptide (BNP) and N-terminal pro-brain natriuretic peptide (NT-proBNP) in the management of children with CHD has increased. There are, however, no current guidelines for their routine use. The aim of this review article is to provide an update on the data regarding the use of BNP/NT-proB...

journal_title：Cardiology in the young

authors： Cantinotti M,Walters HL,Crocetti M,Marotta M,Murzi B,Clerico A

更新日期：2015-03-01 00:00:00

abstract：BACKGROUND:Percutaneous closure of patent ductus arteriosus has become the treatment of choice in many centres. In patients with large ducts and pulmonary hypertension, transcatheter closure has been achieved with success using the Amplatzer Duct Occluder or even the Amplatzer Muscular Ventricular Septal Defect Occlude...

journal_title：Cardiology in the young

authors： García-Montes JA,Camacho-Castro A,Sandoval-Jones JP,Buendía-Hernández A,Calderón-Colmenero J,Patiño-Bahena E,Zabal C

更新日期：2015-03-01 00:00:00

abstract：OBJECTIVE:Protocols for the placement of temporary pacing wires vary among institutions. Our current protocol is to selectively place temporary pacing wires in those patients who develop haemodynamically significant intra-operative arrhythmia. We wished to identify how effective our current protocol is at identifying w...

journal_title：Cardiology in the young

authors： Piggott K,Nehgme R,Decampli W,Pourmoghadam K,Fakioglu H,Blanco C

更新日期：2015-03-01 00:00:00